A Intresting Case of Struge Weber Syndrome
Vikram Vikhe *
Department of General Medicine, Dr. D. Y. Patil Medical College, Hospital & Research Centre, D. Y. Patil Vidyapeeth, Pimpri Pune 18, India.
Prakash Shende
Department of General Medicine, Dr. D. Y. Patil Medical College, Hospital & Research Centre, D. Y. Patil Vidyapeeth, Pimpri Pune 18, India.
Harish Choudhari
Department of General Medicine, Dr. D. Y. Patil Medical College, Hospital & Research Centre, D. Y. Patil Vidyapeeth, Pimpri Pune 18, India.
Ridhima Jakotia
Department of General Medicine, Dr. D. Y. Patil Medical College, Hospital & Research Centre, D. Y. Patil Vidyapeeth, Pimpri Pune 18, India.
*Author to whom correspondence should be addressed.
Abstract
Struge Weber Syndrome is a rare neurocutaneous disorder characterized by Leptomeninigeal & facial angiomas mainly in the course of ophthalmic& maxillary branches of the trigeminal nerve. We report a case of 14 year old male who presented with left hemiparesis since 2 to 3months & Generalized tonic clonic seizures since 5days.Diagnosis is confirmed by CT/MRI. The classical findings seen on CT/MRI are atrophy and calcification of the cerebral hemisphere. The most common neurological symptom seen are seizures, they are typically focal tonic clonic seizures, seen during first year of life. They are often refractory to anti-convulsants. Most children present with slowly progressive hemiparesis during the course of illness.
Keywords: Struge Weber Syndrome, angiomas, seizures, CT / MRI